Total anomalous connection of pulmonary veins to the portal vein. Value of multislice angiotomography. Report on three cases

  • Sara Alejandra Solórzano-Morales Instituto Nacional de Pediatría
  • Francisco Javier López-Elías Instituto Nacional de Pediatría
  • Javier Horacio López-Terrazas Instituto Nacional de Pediatría
  • Max Alberto Bernal-Moreno Instituto Nacional de Pediatría
  • Alexis Javier Palacios-Macedo-Quenot Instituto Nacional de Pediatría
  • Alfredo Bobadilla-Aguirre Instituto Nacional de Pediatría

Resumen

Objective: Present tomographic data from the patients with emphasis
on structural characteristics.
Material and method: Retrospective study of three patients in whom the
four pulmonary veins connected to the portal vein. This malformation is
one of the varieties of total anomalous connection of pulmonary veins.
In any of them, the pulmonary veins do not connect to the left atrium
and blood from the lung reaches the right atrium directly or through
its tributary systems. In such cases, arterialized pulmonary blood and
systemic venous blood mix at the site of the anomalous connection and
a short circuit is formed from the right atrium to the left atrium through
an interauricular communication, allowing patients to survive.
Total anomalous connection of pulmonary veins accounts for between
0.4 and 2.0% of congenital heart diseases: it occurs in 6.8 of every
100,000 individuals. It is diagnosed in 68% of patients in neonatal stage,
which reflects the severity of the condition. The infracardiac variety of
total anomalous connection of pulmonary veins accounts for between
15 and 26% if all its varieties. Multislice angiotomography allows us to view the blood vessels and adjacent organs under consideration and obtain high-definition anatomic information. In the patients in this study, total anomalous connection of pulmonary veins to the portal vein was viewed with three-dimensional volumetric tomographic reconstructions and their correlation with ultrasonography studies.

Biografía del autor/a

Sara Alejandra Solórzano-Morales, Instituto Nacional de Pediatría
Radiology Service
Francisco Javier López-Elías, Instituto Nacional de Pediatría
Radiology Service
Javier Horacio López-Terrazas, Instituto Nacional de Pediatría
Cardiovascular Surgery
Max Alberto Bernal-Moreno, Instituto Nacional de Pediatría
Radiology Service
Alexis Javier Palacios-Macedo-Quenot, Instituto Nacional de Pediatría
Cardiovascular Surgery
Alfredo Bobadilla-Aguirre, Instituto Nacional de Pediatría
Cardiology Service

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Publicado
2014-07-09
Cómo citar
Solórzano-Morales, S., López-Elías, F., López-Terrazas, J., Bernal-Moreno, M., Palacios-Macedo-Quenot, A., & Bobadilla-Aguirre, A. (2014). Total anomalous connection of pulmonary veins to the portal vein. Value of multislice angiotomography. Report on three cases. Acta Pediátrica De México, 35(1), 22-29. https://doi.org/10.18233/APM35No1pp19-25
Sección
Artículo original